Product Description
| Cat Number | T4887 |
|---|---|
| Category | Biochemical |
| Pack Size | 1EA |
| Description | 3-Amino-2-methylpropanoic acid (α-Methyl-β-alanine) is the product from the conversion of N-carbamyl-beta-aminoisobutyric acid by the enzyme Beta-ureidopropionase (EC 3.5.1.6), the last step in pyrimidine degradation. Beta-ureidopropionase deficiency is an inborn error of pyrimidine degradation associated with neurological abnormalities. |
| Molecular Weight | 103.12 |
| Purity | ≥98% |
| Formula | C4H9NO2 |
| Smiles | CC(CN)C(O)=O |
| Storage | -20 ℃ |
| View Document | |
| Note | This product is for Research Use Only |

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